Mucous membrane pemphigoid pdf free

Other diseases that produce the latter pattern linear band on. Mucous membrane pemphigoid is a rare autoimmune blistering disease primarily affecting mucosal surfaces. Blistering and scarring may occur in the eyes, mouth, esophagus, larynx, and on the vulva. Like other forms of pemphigoid, the disorder is characterized by the formation of autoantibodies against structural proteins of the dermalepidermal junction. Treatment strategies in mucous membrane pemphigoid article pdf available in therapeutics and clinical risk management 43. Mucous membrane pemphigoid genetic and rare diseases. Levine early diagnosis and aggressive local and systemic therapy are critical to longterm visual outcome in cases of.

Mucous membrane pemphigoid is a rare, chronic, blistering and scarring disease that affects the oral and ocular mucosa. Mucous membrane pemphigoid mmp this form of the disease affects the eyes, mouth, and throat. Other names include cicatricial pemphigoid, oral pemphigoid and ocular pemphigoid. Scarring can result in severe structural changes to the vulva that may mimic the. Various basement membrane zone components have been identified as targets of. Abstract lichen planus pemphigoides lpp is a rare autoimmune subepidermal blistering disease characterized by the coexistence of both lichen planus and bullous pemphigoid or mucous membrane pemph. Mucous membrane pemphigoid mmp is an autoimmune blistering disorder that is characterized by subepithelial bullae. Other moist surfaces of the body known as mucous membranes can. A clinical formocular cicatricial pemphigoid ocpmay result in blindness if it involves the eyes. Outcomes for mucous membrane pemphigoid depend on early. Bullous pemphigoid bp this strain is limited to the skin. To be a member of this group you must have a form of pemphigoid or an associated illness or be a supporter.